Version 2.80

Part Description

LP31555-3   Sulfocysteine
Cysteine-S-sulfate (SSC) is produced by reaction of inorganic sulfite and cystine by a yet unknown pathway and is a very potent NMDA-receptor agonist. Electrophysiological studies have shown that SSC displays depolarizing properties similar to glutamate. Patients affected with either Molybdenum cofactor deficiency (MOCOD, an autosomal recessive disease that leads to a combined deficiency of the enzymes sulphite oxidase, an enzyme that catalyzes the conversion of sulfite to inorganic sulfate, xanthine dehydrogenase and aldehyde oxidase) or isolated sulphite oxidase deficiency (ISOD, an extremely rare autosomal recessive disorder with identical clinical manifestations to MOCOD) excrete elevated levels of SSC. This rare disorder is associated with brain damage (seizures, spastic quadriplegia, and cerebral atrophy), mental retardation, dislocated ocular lenses, blindness, and excretion in the urine of abnormally large amounts of SSC, sulfite, and thiosulfate but no inorganic sulfate. PMID: 17764028, PMID: 15558695. Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database , Sulfocysteine

Fully-Specified Name

Component
Sulfocysteine
Property
SCnc
Time
Pt
System
CSF
Scale
Qn
Method

Additional Names

Long Common Name
Sulfocysteine [Moles/volume] in Cerebral spinal fluid
Short Name
Sulfocysteine CSF-sCnc
Display Name
Sulfocysteine (CSF) [Moles/Vol]
Consumer Name Alpha Get Info
Sulfocysteine, Spinal fluid

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.27
Last Updated
Version 2.70 (MIN)
Order vs. Observation
Both

Member of these Panels

LOINC Long Common Name
35507-3 Amino acids panel [Moles/volume] - Cerebral spinal fluid

Language Variants Get Info

Tag Language Translation
de-DE German (Germany) Sulfocystein:Stoffmengenkonzentration:Zeitpunkt:Liquor:Quantitativ:
Synonyms: Zerebrospinalflüssigkeit
el-GR Greek (Greece) Σουλφοκυστεΐνη:SCnc:Pt:ΕΝΥ:Qn:
Synonyms: SCnc Σουλφοκυστεΐνη
es-ES Spanish (Spain) Sulfocisteina:Concentración de sustancia:Punto temporal:Líquido Cefalorraquideo:Qn:
Synonyms: Cuantitativo
es-MX Spanish (Mexico) Sulfocisteína:Concentración de sustancias:Punto temporal:Fluído espinal cerebral:Cuantitativo:
et-EE Estonian (Estonia) Sulfotsüsteiin:SCnc:Pt:CSF:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Liikvor
fr-CA French (Canada) Sulfocystéine:Concentration de substance:Temps ponctuel:LCR:Quantitatif:
fr-FR French (France) Sulfocystéine:Moles/Volume:Ponctuel:Liquide céphalorachidien:Numérique:
fr-BE French (Belgium) Sulfocystéine:Concentration de substance:Temps ponctuel:LCR:Quantitatif:
it-IT Italian (Italy) Sulfocisteina:SCnc:Pt:LCS:Qn:
Synonyms: Chimica Concentrazione di Sostanza Liquido cerebrospinale Punto nel tempo (episodio)
nl-NL Dutch (Netherlands) sulfocysteïne:mol/volume:moment:liquor cerebrospinalis:kwantitatief:
pt-BR Portuguese (Brazil) Sulfocisteina:#N/A:Pt:LCR:Qn:
Synonyms: Cys(SO3H); Substance concentration; Level; Point in time; Random; Cerebral spinal fluid; Spinal Fluid; Cerebrospinal Fl; Spinal Flu; Spinal Fld; Quantitative; QNT; Quant; Quan; Chemistry
ru-RU Russian (Russian Federation) Сульфоцистеин:МолКонц:ТчкВрм:ЦСЖ:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Точка во времени;Момент Цереброспинальная жидкость
tr-TR Turkish (Turkey) Sülfosistein:SubKons:Zmlı:BOS:Kant:
zh-CN Chinese (China) 磺酰半胱氨酸:物质的量浓度:时间点:脑脊液:定量型:
Synonyms: CSF CSF;脊髓液;Cerebral spinal fluid;脑脊髓液 Cys(SO3H);犀氨酸 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 脊液 脊髓液 脑脊液（Cerebral spinal fluid，CSF） 脑脊髓液

Example Units

Unit Source
umol/L Example UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=54336-3